A 13-year-old boy, diagnosed with cherubism, had mild exophthalmos and visual acuity (VA) 0.9 on both eyes. Neuroimaging showed multiple cystic images that affected both maxillary and mandibular bones, sparing both mandibular condyles. Cystic formations involved the orbit, causing displacement of the extrinsic muscles and the eyeballs [Fig. 1]. It was decided to monitor him due to the stability of the disease, the mild exophthalmos, the unaffected ocular mobility, and good VA. Cherubism usually starts affecting the jaw, second, the maxilla, and later it may extend to the orbit. Hence, it must be examined by an ophthalmologist to diagnose possible orbital manifestations.[1,2,3,4,5]
Figure 1.
(a and b) Computed tomography (CT) 3D showed bilateral radiolucencies and multicystic lesions in the mandible, maxilla, and orbit. More marked injuries were on the left side. (c) CT Orbital invasion causing exophthalmos. The roofs of the orbits were preserved. (d) Asymmetrical cherubism; it was more marked on the left side. CT: Computed tomography
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