Table 1.

World Health Organization and EORTC classification of PCLs

Classification
Cutaneous T-cell and NK-cell lymphomas
Mycosis fungoides
MF variants and subtypes
Folliculotropic MF
Pagetoid reticulosis
Granulomatous slack skin
Sézary syndrome
Primary cutaneous CD30+ lymphoproliferative disorders
Primary cutaneous anaplastic large cell lymphoma
Lymphomatoid papulosis
Adult T-cell leukemia/lymphoma
Subcutaneous panniculitis–like T-cell lymphoma
Extranodal NK/T-cell lymphoma, nasal type
Chronic active EBV infection
Primary cutaneous peripheral T-cell lymphoma, rare subtypes
Primary cutaneous γ/δ T-cell lymphoma
Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma (provisional)
Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (provisional)
Primary cutaneous acral CD8+ T-cell lymphoma (provisional)
Primary cutaneous peripheral T-cell lymphoma, NOS
Cutaneous B-cell lymphomas
Primary cutaneous marginal zone lymphoma
Primary cutaneous follicle center lymphoma
Primary cutaneous diffuse large B-cell lymphoma, leg type
EBV+ mucocutaneous ulcer (provisional)
Intravascular large B-cell lymphoma

Based on Willemze et al.²

NK, natural killer; EBV, Epstein-Barr virus.