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. 1977 Dec;30(12):1134–1141. doi: 10.1136/jcp.30.12.1134

'Pseudocirrhosis' in hereditary haemorrhagic telangiectasia.

T Cooney, E C Sweeney, R Coll, M Greally
PMCID: PMC476696  PMID: 203609

Abstract

Telangiectasia-associated hepatic fibrosis (TAHF) in a 68-year-old woman with hereditary haemorrhagic telangiectasia (HHT) is described. The patient died of oat-cell carcinoma of the lung. In addition to the structural alterations which have been described previously in HHT, the liver exhibited focal midlobular hepatocytic necrosis and tumour metastases. The possibility that treatment of HHT was causally related to some of the hepatic abnormalities found in our patient and the differentiation of TAHF from true cirrhosis are discussed.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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