We wish to point out that in otological terms, Cogan’s syndrome presents primarily as recurrent, sometimes bilateral, episodes of sudden acute sensorineural hearing loss. These episodes, which may improve initially after intravenous administration of steroids, may result in progressive hearing loss and permanent surdity. In such a scenario, a cochlear implant is the only option to restore a patient’s hearing. We also ask that current terminology be used regarding surdity (“loss of hearing” rather than “deafness” [Box 2], Muckle-Wells syndrome).
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