Abstract
A family is presented with autosomal dominant progressive palmoplantar hyperkeratosis, which is invariably associated with a slowly progressive, bilateral, high frequency, sensorineural hearing loss. The family show no other ectodermal abnormality. The differential diagnosis and possible mechanisms are discussed. This family appears to represent a unique variant in the hyperkeratosis-deafness association.
Full text
PDFImages in this article
Selected References
These references are in PubMed. This may not be the complete list of references from this article.
- Bititci O. O. Familial hereditary, progressive sensori-neural hearing loss with keratosis palmaris and plantaris. J Laryngol Otol. 1975 Nov;89(11):1143–1146. doi: 10.1017/s0022215100081494. [DOI] [PubMed] [Google Scholar]
- Clouston H. R. A Hereditary Ectodermal Dystrophy. Can Med Assoc J. 1929 Jul;21(1):18–31. [PMC free article] [PubMed] [Google Scholar]
- Gibbs R. C., Frank S. B. Keratoma hereditaria mutilans (Vohwinkel). Differentiating features of conditions with constriction of digits. Arch Dermatol. 1966 Nov;94(5):619–625. doi: 10.1001/archderm.94.5.619. [DOI] [PubMed] [Google Scholar]