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Journal of Neurology, Neurosurgery, and Psychiatry logoLink to Journal of Neurology, Neurosurgery, and Psychiatry
. 1985 Oct;48(10):1037–1048. doi: 10.1136/jnnp.48.10.1037

A dominantly inherited lower motor neuron disorder presenting at birth with associated arthrogryposis.

P Fleury, G Hageman
PMCID: PMC1028545  PMID: 4056805

Abstract

Of a family consisting of 54 members, 44 were examined. Twenty-one showed signs of a clinically non-progressive congenital lower motor neuron disorder restricted to the lower part of the body, which resulted in arthrogryposis in 15 cases. The mode of inheritance is autosomal dominant with very varied expression of the gene.

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Selected References

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