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. 1984 Feb;68(2):69–78. doi: 10.1136/bjo.68.2.69

Supernormal scotopic ERG in cone dystrophy.

K R Alexander, G A Fishman
PMCID: PMC1040261  PMID: 6607068

Abstract

Three patients with a bull's-eye macular lesion and other signs characteristic of cone dystrophy gave an unusual ERG finding. In response to a white flash of moderate intensity the scotopic b-wave amplitude was considerably larger than normal. One patient had elevated rod thresholds and nyctalopia, while the other 2 had normal rod sensitivity associated with the supernormal scotopic b-wave amplitude. In the latter 2 patients the abnormal ERG pattern was unchanged for 4 years and 7 years respectively. This atypical finding, of a supernormal scotopic b-wave amplitude in response to light of moderate intensity, appears to characterise a subgroup of patients with cone dystrophy, probably of autosomal recessive inheritance. The pathogenesis of the abnormal ERG remains uncertain.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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