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. 1987 Feb;71(2):130–144. doi: 10.1136/bjo.71.2.130

Congenital hereditary corneal oedema of Maumenee: its clinical features, management, and pathology.

C M Kirkness, A McCartney, N S Rice, A Garner, A D Steele
PMCID: PMC1041104  PMID: 3548808

Abstract

The clinical and histological features of congenital hereditary corneal oedema in 23 patients are presented. The series includes cases of both recessive and dominant inheritance. Although the condition is present at birth or in early childhood, visual development appears to be little impaired, if at all. Penetrating keratoplasty carries a relatively good surgical prognosis and can produce a substantial visual gain even when carried out late in life.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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