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. 1990 Dec;74(12):706–708. doi: 10.1136/bjo.74.12.706

Photic sneeze reflex in nephropathic cystinosis.

B Katz 1, R B Melles 1, M R Swenson 1, J A Schneider 1
PMCID: PMC1042271  PMID: 2275931

Abstract

Photic induced sneeze is a reflex that occurs in certain individuals after exposure to bright light. Cystinosis is an autosomal recessive inborn error of metabolism in which nonprotein cystine accumulates within lysosomes. The pathognomonic ocular manifestation of cystinosis is corneal crystal deposition. We observed photic induced sneezes during ophthalmoscopic examination in five of 19 patients with nephropathic cystinosis (26%). We report on this observation and discuss possible pathophysiological mechanisms for photic induced sneezing in cystinosis.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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