Abstract
A patient with pseudoxanthoma elasticum presented in pulmonary oedema with restrictive left ventricular cardiomyopathy caused by calcified endocardial bands that were confirmed on echocardiography and at catheterisation. The bands were resected as far as possible and the involved mitral valve was replaced by a heterograft. A year later calcification of the heterograft forced its replacement by a St Jude prosthesis. Relief of symptoms has been good in the medium term.
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- Bete J. M., Banas J. S., Jr, Moran J., Pinn V., Levine H. J. Coronary artery disease in an 18 year old with pseudoxanthoma elasticum: successful surgical therapy. Am J Cardiol. 1975 Oct 6;36(4):515–520. doi: 10.1016/0002-9149(75)90904-2. [DOI] [PubMed] [Google Scholar]
- COFFMAN J. D., SOMMERS S. C. Familial pseudoxanthoma elasticum and valvular heart disease. Circulation. 1959 Feb;19(2):242–250. doi: 10.1161/01.cir.19.2.242. [DOI] [PubMed] [Google Scholar]
- Huang S. N., Steele H. D., Kumar G., Parker J. O. Ultrastructural changes of elastic fibers in pseudoxanthoma elasticum. A study of histogenesis. Arch Pathol. 1967 Jan;83(1):108–113. [PubMed] [Google Scholar]
- Lebwohl M. G., Distefano D., Prioleau P. G., Uram M., Yannuzzi L. A., Fleischmajer R. Pseudoxanthoma elasticum and mitral-valve prolapse. N Engl J Med. 1982 Jul 22;307(4):228–231. doi: 10.1056/NEJM198207223070406. [DOI] [PubMed] [Google Scholar]
- Navarro-Lopez F., Llorian A., Ferrer-Roca O., Betriu A., Sanz G. Restrictive cardiomyopathy in pseudoxanthoma elasticum. Chest. 1980 Jul;78(1):113–115. doi: 10.1378/chest.78.1.113. [DOI] [PubMed] [Google Scholar]
- Przybojewski J. Z., Daniels A. R., Van der Walt J. J. Primary cardiac amyloidosis: A case presentation. S Afr Med J. 1980 May 10;57(19):774–780. [PubMed] [Google Scholar]
- Przybojewski J. Z., Maritz F., Tiedt F. A., van der Walt J. J. Pseudoxanthoma elasticum with cardiac involvement. A case report and review of the literature. S Afr Med J. 1981 Feb 21;59(8):268–275. [PubMed] [Google Scholar]
- Voelkel A. G., Pietro D. A., Folland E. D., Fisher M. L., Parisi A. F. Echocardiographic features of constrictive pericarditis. Circulation. 1978 Nov;58(5):871–875. doi: 10.1161/01.cir.58.5.871. [DOI] [PubMed] [Google Scholar]
- Wilhelm K., Paver K. Sudden death in pseudoxanthoma elasticum. Med J Aust. 1972 Dec 9;2(24):1363–1365. doi: 10.5694/j.1326-5377.1972.tb92932.x. [DOI] [PubMed] [Google Scholar]