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Journal of the Royal Society of Medicine logoLink to Journal of the Royal Society of Medicine
. 1995 Jun;88(6):357P–358P.

Adult-onset congenital erythropoietic porphyria (Günther's disease) presenting with thrombocytopenia.

A Murphy 1, G Gibson 1, G H Elder 1, B A Otridge 1, G M Murphy 1
PMCID: PMC1295249  PMID: 7629774

Abstract

Cutaneous signs of Günther's disease (congenital erythropoietic porphyria) developing 5 years after the onset of symptomatic thrombocytopenia are described in a 65-year-old man. Persistent thrombocytopenia unresponsive to corticosteroids and immunoglobulin necessitated a splenectomy.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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