Skip to main content
Journal of the Royal Society of Medicine logoLink to Journal of the Royal Society of Medicine
. 1995 Jun;88(6):357P–358P.

Adult-onset congenital erythropoietic porphyria (Günther's disease) presenting with thrombocytopenia.

A Murphy 1, G Gibson 1, G H Elder 1, B A Otridge 1, G M Murphy 1
PMCID: PMC1295249  PMID: 7629774

Abstract

Cutaneous signs of Günther's disease (congenital erythropoietic porphyria) developing 5 years after the onset of symptomatic thrombocytopenia are described in a 65-year-old man. Persistent thrombocytopenia unresponsive to corticosteroids and immunoglobulin necessitated a splenectomy.

Full text

PDF
357P

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Haining R. G., Cowger M. L., Shurtleff D. B., Labbe R. F. Congenital erythropoietic porphyria. I. Case report, special studies and therapy. Am J Med. 1968 Oct;45(4):624–637. doi: 10.1016/0002-9343(68)90177-0. [DOI] [PubMed] [Google Scholar]
  2. Horiguchi Y., Horio T., Yamamoto M., Tanaka T., Seki Y., Imamura S. Late onset erythropoietic porphyria. Br J Dermatol. 1989 Aug;121(2):255–262. doi: 10.1111/j.1365-2133.1989.tb01808.x. [DOI] [PubMed] [Google Scholar]
  3. Kramer S., Viljoen E., Meyer A. M., Metz J. The anaemia of erythropoietic prophyria with the description of the disease in an elderly patient. Br J Haematol. 1965 Nov;11(6):666–675. doi: 10.1111/j.1365-2141.1965.tb00115.x. [DOI] [PubMed] [Google Scholar]
  4. MacDonald A., Nicholson D., Williams R. Late onset erythropoietic uroporphyria. Br J Dermatol. 1976 Jul;95 (Suppl 14):30–33. doi: 10.1111/j.1365-2133.1976.tb07899.x. [DOI] [PubMed] [Google Scholar]
  5. Pain R. W., Welch F. W., Woodroffe A. J., Handley D. A., Lockwood W. H. Erythropoietic uroporphyria of Gunther first presenting at 58 years with positive family studies. Br Med J. 1975 Sep 13;3(5984):621–623. doi: 10.1136/bmj.3.5984.621. [DOI] [PMC free article] [PubMed] [Google Scholar]
  6. Rank J. M., Straka J. G., Weimer M. K., Bossenmaier I., Taddeini B. L., Bloomer J. R. Hematin therapy in late onset congenital erythropoietic porphyria. Br J Haematol. 1990 Aug;75(4):617–618. doi: 10.1111/j.1365-2141.1990.tb07809.x. [DOI] [PubMed] [Google Scholar]

Articles from Journal of the Royal Society of Medicine are provided here courtesy of Royal Society of Medicine Press

RESOURCES