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. 1970 Dec;11(12):983–988. doi: 10.1136/gut.11.12.983

Hereditary angioneurotic oedema: an unusual case of recurring abdominal pain 1

Edward J Feller, Howard M Spiro, Leonard A Katz
PMCID: PMC1553179  PMID: 5511819

Abstract

Two patients with hereditary angioneurotic oedema, a condition characterized by repeated episodes of abdominal pain and oedema, and by an absence of complement-1 esterase inhibitor activity in the plasma are presented in detail. Both underwent multiple surgical procedures before the diagnosis was established. Abdominal pain is often the presenting complaint, and although a complete history will usually lead to the proper diagnosis, cases in which the family history is not clear can present a diagnostic dilemma. Characteristic radiological demonstration of localized intestinal oedema will only be obtained if studies are performed early during the acute attack.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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