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. 2000 Dec;84(6):674–678. doi: 10.1136/heart.84.6.674

Cardiovascular surgery for Marfan syndrome

T Treasure 1
PMCID: PMC1729522  PMID: 11083754

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Figure 1:  .

Figure 1:  

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Histological appearance of a Marfan aorta. On the left is the severe form of medial degeneration called "cystic medial necrosis".

Figure 2:  .

Figure 2:  

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Classification of aortic dissection by the simpler dichotomous Stanford classification (ascending involved or not) and the older DeBakey system.

Figure 3:  .

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The typical form of lethal dissection, which is the most common cause of death in Marfan syndrome.

Figure 4:  .

Figure 4:  

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Operations for aortic dissection or ascending aortic replacement. (A) Simple tube replacement of the aorta for the sinotubular junction to the brachiocephalic origin. (B) Tube graft replacement and aortic valve replacement as separate components of the operation. (C) Composite graft replacement. (D) Leaflet sparing aortic root replacement.

Figure 5:  .

Figure 5:  

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Points of echo measurement for surveillance of the aortic root. The diameter of the aortic root can be measured at three different levels. In Marfan syndrome level B is critical.

Figure 6:  .

Figure 6:  

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A patient who showed no increase in aorta size from the age of 44 to 54 years and an aortic dimension of around 40 mm. This patient does not reach any of our current criteria for root replacement.

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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