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. 1978 Sep;54(635):618–622. doi: 10.1136/pgmj.54.635.618

A case of multiple endocrine adenomatosis with primary amenorrhoea.

M Vandeweghe, K Braxel, J Schutyser, A Vermeulen
PMCID: PMC2425223  PMID: 31610

Abstract

A well documented sporadic case of multiple endocrine adenomatosis (MEA) type I, with the pituitary tumour presenting as a prolactinoma, is described in a 28-year-old female. Primary amenorrhoea, resulting from hyperprolactinaemia, was the first symptom of the polyglandular neoplasia. A gastrinoma was removed from the head of the pancreas and latent hyperparathyroidism appeared to be present. Treatment with bromocriptine was poorly tolerated; neurosurgical intervention was refused by the patient. The possibility that a serum prolactin determination may be useful in detecting pituitary involvement in MEA deserves consideration.

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Selected References

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