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. 1977 Jan;27(1):23–29.

A second case of human C3b inhibitor (KAF) deficiency.

R A Thompson, P J Lachmann
PMCID: PMC1540911  PMID: 849647

Abstract

The second case of C3b inhibitor deficiency is described in an 11-year-old girl who presented with recurrent attacks of meningitis, in between which she was well. Her serum showed all of the complement component changes noted in the first described case, although showing only a relatively slight defect in its ability to opsonize bacteria for phagocytosis and killing by polymorphonuclear leucocytes. This correlated with the patient's freedom from other infections.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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