Skip to main content
British Heart Journal logoLink to British Heart Journal
. 1979 May;41(5):544–553. doi: 10.1136/hrt.41.5.544

Nomenclature and classification of congenital heart disease.

M J Tynan, A E Becker, F J Macartney, M Q Jiménez, E A Shinebourne, R H Anderson
PMCID: PMC482068  PMID: 465224

Abstract

At present there is no universally accepted nomenclature for congenital cardiac malformations. Much of the controversy results from failure to distinguish the structural connections of the heart from the morphology and spatial relations of its components. The confusion is compounded by an abundance of individual definitions, many of them speculative. The present article proposes a totally descriptive nomenclature. It describes in turn the connections of the cardiac segments, their morphology, their relations, and additional anomalies in any segment. Each step in the segmental approach is discrete. The overall effect is to force a succinct and comprehensive description of any cardiac malformation, no matter how complex.

Full text

PDF
544

Images in this article

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Anderson R. H., Wilkinson J. L., Gerlis L. M., Smith A., Becker A. E. Atresia of the right atrioventricular orifice. Br Heart J. 1977 Apr;39(4):414–428. doi: 10.1136/hrt.39.4.414. [DOI] [PMC free article] [PubMed] [Google Scholar]
  2. Brandt P. W., Calder A. L. Cardiac connections: the segmental approach to radiologic diagnosis in congenital heart disease. Curr Probl Diagn Radiol. 1977 May-Jun;7(3):1–35. doi: 10.1016/s0363-0188(77)80006-6. [DOI] [PubMed] [Google Scholar]
  3. Kirklin J. W., Pacifico A. D., Bargeron L. M., Jr, Soto B. Cardiac repair in anatomically corrected malposition of the great arteries. Circulation. 1973 Jul;48(1):153–159. doi: 10.1161/01.cir.48.1.153. [DOI] [PubMed] [Google Scholar]
  4. LEV M. Pathologic diagnosis of positional variations in cardiac chambers in congenital heart disease. Lab Invest. 1954 Jan-Feb;3(1):71–82. [PubMed] [Google Scholar]
  5. Lev M., Liberthson R. R., Kirkpatrick J. R., Eckner F. A., Arcilla R. A. Single (primitive) ventricle. Circulation. 1969 May;39(5):577–591. doi: 10.1161/01.cir.39.5.577. [DOI] [PubMed] [Google Scholar]
  6. Liberthson R. R., Paul M. H., Muster A. J., Arcilla R. A., Eckner F. A., Lev M. Straddling and displaced atrioventricular orifices and valves with primitive ventricles. Circulation. 1971 Feb;43(2):213–226. doi: 10.1161/01.cir.43.2.213. [DOI] [PubMed] [Google Scholar]
  7. Macartney F. J., Partridge J. B., Scott O., Deverall P. B. Common or single ventricle. An angiocardiographic and hemodynamic study of 42 patients. Circulation. 1976 Mar;53(3):543–554. doi: 10.1161/01.cir.53.3.543. [DOI] [PubMed] [Google Scholar]
  8. Mortera C., Hunter S., Terry G., Tynan M. Echocardiography of primitive ventricle. Br Heart J. 1977 Aug;39(8):847–855. doi: 10.1136/hrt.39.8.847. [DOI] [PMC free article] [PubMed] [Google Scholar]
  9. Partridge J. B., Scott O., Deverall P. B., Macartney F. J. Visualization and measurement of the main bronchi by tomography as an objective indicator of thoracic situs in congenital heart disease. Circulation. 1975 Jan;51(1):188–196. doi: 10.1161/01.cir.51.1.188. [DOI] [PubMed] [Google Scholar]
  10. Quero Jiménez M., Pérez Martínez V. M., Maitre Azcárate M. J., Merino Batres G., Moreno Granados F. Exaggerated displacement of the atrioventricular canal towards the bulbus cordis (rightward displacement of the mitral valve). Br Heart J. 1973 Jan;35(1):65–74. doi: 10.1136/hrt.35.1.65. [DOI] [PMC free article] [PubMed] [Google Scholar]
  11. Shinebourne E. A., Macartney F. J., Anderson R. H. Sequential chamber localization--logical approach to diagnosis in congenital heart disease. Br Heart J. 1976 Apr;38(4):327–340. doi: 10.1136/hrt.38.4.327. [DOI] [PMC free article] [PubMed] [Google Scholar]
  12. Stanger P., Rudolph A. M., Edwards J. E. Cardiac malpositions. An overview based on study of sixty-five necropsy specimens. Circulation. 1977 Aug;56(2):159–172. doi: 10.1161/01.cir.56.2.159. [DOI] [PubMed] [Google Scholar]
  13. VANPRAAGH R., ONGLEY P. A., SWAN H. J. ANATOMIC TYPES OF SINGLE OR COMMON VENTRICLE IN MAN. MORPHOLOGIC AND GEOMETRIC ASPECTS OF 60 NECROPSIED CASES. Am J Cardiol. 1964 Mar;13:367–386. doi: 10.1016/0002-9149(64)90453-9. [DOI] [PubMed] [Google Scholar]
  14. Van Mierop L. H., Eisen S., Schiebler G. L. The radiographic appearance of the tracheobronchial tree as an indicator of visceral situs. Am J Cardiol. 1970 Oct;26(4):432–435. doi: 10.1016/0002-9149(70)90743-5. [DOI] [PubMed] [Google Scholar]
  15. Van Praagh R. Terminology of congenital heart disease. Glossary and commentary. Circulation. 1977 Aug;56(2):139–143. doi: 10.1161/01.cir.56.2.139. [DOI] [PubMed] [Google Scholar]
  16. de la Cruz M. V., Berrazueta J. R., Arteaga M., Attie F., Soni J. Rules for diagnosis of arterioventricular discordances and spatial identification of ventricles. Crossed great arteries and transposition of the great arteries. Br Heart J. 1976 Apr;38(4):341–354. doi: 10.1136/hrt.38.4.341. [DOI] [PMC free article] [PubMed] [Google Scholar]
  17. de la Cruz M. V., Nadal-Ginard B. Rules for the diagnosis of visceral situs, truncoconal morphologies, and ventricular inversions. Am Heart J. 1972 Jul;84(1):19–32. doi: 10.1016/0002-8703(72)90301-8. [DOI] [PubMed] [Google Scholar]

Articles from British Heart Journal are provided here courtesy of BMJ Publishing Group

RESOURCES