Abstract
Six patients are described with a history of slowly progressive wasting of the muscle of the hands and forearms extending over periods of up to 20 years. The clinical, radiological, and electrophysiological findings were consistent with a diagnosis of chronic anterior horn cell degeneration. It is suggested that the patients are affected by a form of distal chronic spinal muscular atrophy affecting the hands.
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- DAWSON G. D. The relative excitability and conduction velocity of sensory and motor nerve fibres in man. J Physiol. 1956 Feb 28;131(2):436–451. doi: 10.1113/jphysiol.1956.sp005473. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Dyck P. J., Lambert E. H. Lower motor and primary sensory neuron diseases with peroneal muscular atrophy. II. Neurologic, genetic, and electrophysiologic findings in various neuronal degenerations. Arch Neurol. 1968 Jun;18(6):619–625. doi: 10.1001/archneur.1968.00470360041003. [DOI] [PubMed] [Google Scholar]
- McLeod J. G., Prineas J. W. Distal type of chronic spinal muscular atrophy. Clinical, electrophysiological and pathological studies. Brain. 1971;94(4):703–714. doi: 10.1093/brain/94.4.703. [DOI] [PubMed] [Google Scholar]
- Meadows J. C., Marsden C. D. A distal form of chronic spinal muscular atrophy. Neurology. 1969 Jan;19(1):53–58. doi: 10.1212/wnl.19.1.53. [DOI] [PubMed] [Google Scholar]
- Mulder D. W., Howard F. M., Jr Patient resistance and prognosis in amyotrophic lateral sclerosis. Mayo Clin Proc. 1976 Sep;51(9):537–541. [PubMed] [Google Scholar]