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. 1981 Dec;65(12):859–865. doi: 10.1136/bjo.65.12.859

Sorsby's pseudoinflammatory macular dystrophy.

A Hoskin, K Sehmi, A C Bird
PMCID: PMC1039695  PMID: 7317334

Abstract

Forty-three additional members of a family described originally by Sorsby and Mason have been examined in order to typify pseudoinflammatory macular dystrophy more accurately. Six new affected members were identified by history alone and a further 7 were examined. Vision is lost from disciform macular degeneration generally during the 5th decade of life. Thereafter peripheral degeneration occurs in some affected members. Before loss of vision the fundus changes include fine drusen-like deposits at the level of Bruch's membrane, angioid streaks, and plaque-like deposits of yellow subretinal material in the macular region. These changes are different from those seen in dominant drusen.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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